Dwarfism Research Today is a free monthly online journal that collates and summarizes the latest research about Dwarfism, including details on genetics, diet, mental and motor development.

Bilateral total hip arthroplasty in Morquio-Brailsford's Syndrome: a report of two cases.

Tassinari E, Boriani L, Traina F, Dallari D, Toni A, Giunti A

1st Division. Istituto Ortopedico Rizzoli, Via Pupilli 1, 40136, Bologna, Italy, enrico.tassinari@ior.it.

We report two cases of bilateral cementless total hip arthroplasty in two young women affected by Morquio-Brailsford syndrome. Morquio-Brailsford disease belongs to the mucopolysaccharidoses; it shows growth retardation with disproportional dwarfism. Usually patients are affected by a severe joint degeneration from their 2nd or 3rd decade. Young age, severe dysplasia, and joint size are the main technical problems for a total hip replacement. Accurate radiographic and CT planning allows the use of standard prostheses instead of custom-made ones.

Published 19 May 2008 in Chir Organi Mov.
Full-text of this article is available online (may require subscription).

© 2005-2008 Dwarfism Research Today. All Rights Reserved.